Spinal curvature is a common concern, with scoliosis affecting 60-90% of children with SMA types 1 and 2 and initial presentation in early childhood. This may be addressed by surgical correction or positional support (e.g. bracing). The decision to perform surgical correction of complications such as scoliosis is based on the child’s spine curvature, pulmonary function, and bone maturity.1,2
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SURGERY |
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BRACING |
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References
1. Spinal Muscular Atrophy Clinical Research Center. Physical/occupational therapy. http://columbiasma.org/pt-ot.html. Updated March 14, 2013. Accessed April 18, 2016. 2. Mercuri E, et al. Diagnosis and management of spinal muscular atrophy: Part 1: Recommendations for diagnosis, rehabilitation, orthopedic and nutritional care. Neuromuscl Disord. 2018;28(2):103-115. 3. Mullender M, Blom N, De Kleuver M, et al. A Dutch guideline for the treatment of scoliosis in neuromuscular disorders. Scoliosis. 2008;3:14. 4. Tangsrud SE, Carlsen KC, Lund-Petersen I, Carlsen KH. Lung function measurements in young children with spinal muscular atrophy; a cross sectional survey on the effect of position and bracing. Arch Dis Child. 2001;84(6):521-524.

The clinical spectrum of SMA is highly variable and requires comprehensive medical care involving multiple disciplines.2